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Volume 114, Nº 4, Supplement, April 2020

   

DOI: https://doi.org/10.36660/abc.20180077

CASE REPORT

Transthyretin Amyloidosis (ATTR) - The Role of Multimodality in the Definitive Diagnosis

Tonnison de Oliveira Silva

Eduardo Saad Darzé

Luiz Eduardo Fonteles Ritt

André Luiz Cerqueira Almeida

Antônio Ximenes



Figure 1 – 1-A) Strain echocardiography showing classic apical sparing. 1-B) MRI with diffuse heterogeneous left ventricular late enhancement (arrows on the left) and diffuse increase in LV thickness (arrow on the right). 1-C) Result of genetic study showing valine to isoleucine mutation (VAL142IIe).





Keywords: Amyloidosis/complications; Prealbumin; Cardiomyopathy,Restrictive; Endomyocardial Fibrosis; Hypertension; Heart Failure; Diagnostic Imaging.