Volume 114, Nº 4, Supplement, April 2020
DOI: https://doi.org/10.36660/abc.20190037
CASE REPORT
Glycogen Storage Disease Type I (Von Gierke disease): Report of Two Cases with Severe Dyslipidemia
Julia Maria Avelino Ballavenuto
Jéssica D´Ório Dantas de Oliveira
Renato Jorge Alves
Keywords: Glycogen Strage Disease Type 1/complications; Gluconeogenesis; Dyslipidemias; Hepatomegaly; Hypoglycemia; Glucose-6-Phosphate.