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Volume 114, Nº 4, Supplement, April 2020

   

DOI: https://doi.org/10.36660/abc.20190037

CASE REPORT

Glycogen Storage Disease Type I (Von Gierke disease): Report of Two Cases with Severe Dyslipidemia

Julia Maria Avelino Ballavenuto

Jéssica D´Ório Dantas de Oliveira

Renato Jorge Alves



Keywords: Glycogen Strage Disease Type 1/complications; Gluconeogenesis; Dyslipidemias; Hepatomegaly; Hypoglycemia; Glucose-6-Phosphate.