IJCS | Volume 31, Nº6, November / December 2018

669 Chart 1 - Revised 2010 Task Force Criteria for the Diagnosis of Arrhythmogenic Right Ventricular Dysplasia/ Cardiomyopathy (ARVD) 1. Global or regional dysfunction and structural alterations Major At the two-dimensional echocardiogram: - Regional right ventricular akinesis, dyskinesis or aneurysm And one of the following (end-diastolic): - RVOT PLAX ≥ 32 mm (corrected for the body surface area − PLAX/BSA ≥ 19 mm/m 2 ) - RVOT PSAX ≥ 36 mm (corrected for the body surface area − PLAX/BSA ≥ 21 mm/m 2 ) - Or fractional alteration of the area ≤ 33% At the MRI: - Regional right ventricular akinesis, dyskinesis or dyssynchrony in right ventricular contractions And one of the following: Ratio of right ventricular end-diastolic volume and BSA ≥ 110 mL/m 2 (male) or BSA ≥ 100 mL / m 2 (female) -- Or right ventricular ejection fraction ≤ 40% At the right ventricular angiography: - Right ventricular regional akinesis, dyskinesis or aneurysm Minor At the two-dimensional echocardiogram: - Right ventricular regional akinesis or dyskinesis And one of the following (end-diastolic): - RVOT PLAX ≥ 29 mm and < 32 mm (corrected for the body surface area − PLAX/BSA ≥ 16 mm/m 2 and < 19 mm/m 2 ) - RVOT PSAX ≥ 32 mm and < 36 mm (corrected for the body surface area − PLAX/BSA ≥ 18 mm/m 2 and < 21 mm/m 2 ) - Or fractional alteration of the area > 33% and ≤ 40% At the MRI: - Regional right ventricular akinesis or dyskinesis or dyssynchrony in right ventricular contraction And one of the following: - Ratio of right ventricular end-diastolic volume and BSA ≥ 100 and < 110 mL/m 2 (man) or ≥ 90 and < 100 mL/m 2 (woman) - Or Right ventricular ejection fraction > 40% and ≤ 45% 2. Histological characterization of the ventricular wall Major - Residual myocytes <60% in the morphometric analysis (or <50% by estimation) with fibrous replacement of the right ventricular free wall in more than one sample, with or without adipose replacement in myocardial biopsy Minor - 60-75% of residual myocytes in the morphometric analysis (or 50-65% by estimation) with fibrous replacement of right ventricular free wall in more than one sample, with or without adipose replacement in myocardial biopsy 3. Ventricular repolarization alterations Major - Inverted T waves in V1, V2 or V3 in individuals aged > 14 years in the absence of complete RBBB with QRS ≥ 120 ms Minor - Inverted T waves in V1 and V2 in individuals aged > 14 years in the absence of complete RBBB with QRS ≥ 120 ms or in V4, V5 or V6 Inverted T waves in V1, V2, V3 and V4 in subjects aged > 14 years in the presence of complete RBBB with QRS ≥ 120 ms Augusto et al. Biventricular arrhythmogenic cardiomyopathy Int J Cardiovasc Sci. 2018;31(6)667-671 Case Report