ABC | Volume 112, Nº1, January 2019

Elias Nero et al ARVC/D - Diagnosis and treatment Arq Bras Cardiol. 2019; 112(1):91-103 Review Article Table 1 – Task Force Criteria reviewed 1. Structural changes and global or regional dysfunction Major criteria • Two-dimensional echocardiogram □ Akinesia, dyskinesia or regional RV aneurysm associated with one of the following diastole measures: – PLAX RVOT ≥ 32 mm (PLAX / BSA ≥ 19 mm/m 2 ) or – PSAX RVOT ≥ 36 mm (PSAX/BSA ≥ 21 mm/m 2 ) or – Fractional area change ≤ 33% • CMR □ Akinesia or regional RV dyskinesia or dyssynchronism of RV contraction associated with one of the following measures: – RV EDV/BSA ≥ 110 mL/m 2 (male) or ≥ 100 mL/m 2 (fem.) – RV ejection fraction ≤ 40% • Right ventriculography □ Akinesia, dyskinesia or RV aneurysm Minor criteria • Two-dimensional echocardiogram □ Akinesia, RV dyskinesia or dissyncronism of RV contraction and one of the measures of diastolic function below: – PLAX RVOT ≥ 29 to < 32 mm (PLAX/BSA ≥ 16 to < 19 mm/m 2 ) or – PSAX RVOT ≥ 32 to < 36 mm (PSAX/BSA ≥ 18 to < 21 mm/m 2 ) or – Fractional area change> 33% ≤40% • CMR □ Akinesia or regional RV dyskinesia or dyssynchronism of RV contraction and one of the following measures: – RV EDV/BSA ≥ 100 to 110 mL/m 2 (male) or ≥ 90 to 100 mL/m 2 (fem.) – RV ejection fraction > 40 to ≤ 45% 2. Tissue aspects Major criteria • Residual myocyte count <60% by morphometric analysis (or <50%, if estimated), with fibrous RV free wall replacement in ≥1 sample, with or without fat replacement of endomyocardial biopsy tissue Minor criteria • Residual myocyte count of 60% to 75% by morphometric analysis (or 50% to 65% if estimated), with fibrous RV free wall replacement in ≥1 sample, with or without fat replacement of endomyocardial biopsy tissue 3. Repolarization abnormalities Major criteria • Inverted T waves in the right precordial vessels (V1, V2, and V3) or extending beyond V3 in individuals > 14 years of age (in the absence of RBBB-QRS ≥ 120 ms) Minor criteria • Inverted T waves in V1 and V2 in ind. > 14 years of age (in the absence of RBBB) • Inverted T waves in V1, V2, V3, AND V4 in ind. > 14 years, in the presence of RBBB 4. Depolarization / conduction abnormalities Major criteria • Epsilon wave (reproducible low amplitude signals between the end of the QRS and the beginning of the T wave) in the right precordial leads (V1 - V3) Minor criteria • Late potentials on the ECG-HR in ≥ 1 of the 3 parameters in the absence of QRSd ≥ 110 msec in the 12-lead ECG: □ Filtered QRS duration (fQRS) ≥ 114 msec □ Duration of terminal QRS < 40 micro V ≥ 38 ms □ Root-mean-square voltage of terminal 40 ms ≤ 20 micro V • Duration of the final QRS portion ≥ 55 ms (measurement of nadir from S wave to end of ventricular depolarization - including R’) in V 1, V 2 or V 3 4