ABC | Volume 110, Nº2, February 2018

Case Report Lopes et al. Fetal ARV dysplasia Arq Bras Cardiol. 2018; 110(2):201-202 Figure 1 – Fetal echocardiography and anatomic features observed at the autopsy. (a) Four-chamber view at 36 weeks showing cardiac enlargement and left atrial dilatation. (b) Three-vessel view showing reversal flow at the ductus arteriosus level (arrow). (c) Heart and lungs with pale, enlarged right ventricle. (d) Right ventricular wall is thin and almost devoid of muscle fibers. (e) A hematoxylin-eosin stain demonstrating absence of myocardial fibers and fibrofatty tissue replacement of the anterior free wall of the right ventricle. RA: right atrium; RV: right ventricle; LA: left atrium; LV: left ventricle; L: lungs. 1. Basso C, Corrado D, Marcus FI, Nava A, Thiene G. Arrhythmogenic right ventricular cardiomyopathy. Lancet. 2009;373(9671):1289-300. 2. RusticoMA,BenettoniA,FontaliranF,FontaineF.Prenatalechocardiographic appearance of arrhythmogenic right ventricle dysplasia: a case report. Fetal Diagn Ther. 2001;16(6):433-6. 3. FalkensammerCB,Paul J,Huhta JC.Fetalcongestiveheart failure:correlation of Tei-index and cardiovascular score. J Perinat Med. 2001;29(5):390-8. 4. Marcus FI, McKenna WJ, Sherrill D, Basso C, Bauce B, Bluemke DA, et al. Diagnosis of arrhythmogenic right ventricular cardiomyopathy/ dysplasia: proposed modification of the task force criteria. Circulation. 2010;121(13):1533-41. 5. Lindström L, Wilkenshoff UM, Larsson H, Wranne B. Echocardiographic assessment of arrhythmogenic right ventricular cardiomyopathy. Heart. 2001;86(1):31-8. 6. McKennaWJ,ThieneG,NavaA,FontaliranF,Blomstrom-LundquistG,FontaineG, etal.Diagnosisofarrhythmogenicrightventriculardysplasia/cardiomyopathy.Task ForceoftheWorkingGroupMyocardialandPericardialDiseaseoftheEuropean Society of Cardiology and of the Scientific Council on Cardiomyopathies of the InternationalSocietyandFederationofCardiology.BrHeartJ.1994;71(3):215-8. References this case the evolution to cardiac failure and death could not be prevented, but we should be very careful when analyzing fetal rhythm, since a correct prenatal diagnosis is crucial for selecting the correct antiarrhythmic treatment and improve chances of survival. This article not only teaches us about the importance of echocardiographic ventricular function evaluation, especially in case of ventricular arrhythmia, but also highlights ARVD as a possible diagnosis in the fetus in early pregnancy. Author contributions Conception and design of the research and Analysis and interpretation of the data: Lopes LM; Acquisition of data: Lopes LM, Pacheco JT, Schultz R; Writing of the manuscript: Lopes LM, Pacheco JT; Critical revision of the manuscript for intellectual content: Lopes LM, Schultz R, Francisco RPV, Zugaib M. Potential Conflict of Interest No potential conflict of interest relevant to this article was reported. Sources of Funding There were no external funding sources for this study. Study Association This study is not associatedwith any thesis or dissertationwork. This is an open-access article distributed under the terms of the Creative Commons Attribution License 202